Fırat Üniversitesi Sağlık Bilimleri Tıp Dergisi |
2007, Cilt 21, Sayı 2, Sayfa(lar) 091-094 |
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Anaesthesia application in two siblings with mucopolysaccharidoses |
Ayşe Belin ÖZER, Azize BEŞTAŞ, Ömer Lütfi ERHAN, Mustafa Kemal BAYAR, Hülya GÖKSU |
Fırat Universitesi Tıp Fakültesi, Anestezi ve Reanimasyon Anabilim Dalı Elazığ -TÜRKİYE |
Keywords: mucopolysaccharidoses, Anaesthesia |
Mucopolysaccharidosis is a rare otosomal recessive metabolic condition. The clinical
differentations developed in organs and systems are especially due to dermatan and heparan
sulfat accumulation. The condensation of these alterations in muscle-skeletal, cardiovascular,
respiration and internal organs lead to problems about anaesthesia. Heart insufficiency,rhythm
disorders and pulmonary oedema occur as weel as difficulty in airway supply.Before after and
during anaesthesia must be well prepared with this respect.
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[ Turkish ]
[ Tam Metin ]
[ PDF ]
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