Choroid plexus papillomas are rare neuroectodermal tumors that develop from choroid plexus epithelial cells and grow up intraventricular. Most of intraventricular tumors are slow-growing low grade tumors and progress insidiously until they are result in hydrocephalus and increassed intracranial pressure syndrome by obstruct to cerebrospinal fluid circulation. Therefore they may grow up to huge volume without symptom and usually require to emergency intervention. They sometimes threaten the life of sufferer by obstructing cerebrospinal circulation suddenly. In this case report, we presented a case of fourth ventricle choroid plexus papilloma presenting with migraine-like headache and reviewed related literature.